MUKOVISTSIDOZ KASALLIGIDA NAFAS TIZIMI FAOLIYATINING BUZILISHI VA UNI REABILITATSIYA QILISH USULLARI

Authors

  • Karimkulova Gulshonoy Akmaljon qizi Author

Abstract

Mukovistsidoz – bu avtosomal-retsessiv yo‘l bilan irsiy tarzda o‘tuvchi og‘ir 
surunkali  kasallik  bo‘lib,  u  organizmning  ko‘pgina  hayotiy  muhim  organlarida, 
ayniqsa o‘pka va me’da osti bezida yopishqoq va qalin sekresiyaning to‘planishi bilan 
xarakterlanadi. Bu holat, asosan, CFTR (Cystic Fibrosis Transmembrane Conductance 
Regulator)  genidagi  mutatsiyalar  bilan  bog‘liq  bo‘lib,  natijada  natriy  va  xlor 
ionlarining hujayralararo almashinuvida buzilish yuzaga keladi[1]. 

References

FOYDALANILGAN ADABIYOTLAR

1. Ratjen F, Döring G. Cystic fibrosis. Lancet. 2003;361(9358):681–689.

doi:10.1016/S0140-6736(03)12567-6

2. Flume PA et al. Cystic fibrosis pulmonary guidelines: airway clearance therapies.

Respir Care. 2009;54(4):522–537.

3. Gibson RL, Burns JL, Ramsey BW. Pathophysiology and management of

pulmonary infections in cystic fibrosis. Am J Respir Crit Care Med.

2003;168(8):918–951.

4. Elborn JS. Cystic fibrosis. Lancet. 2016;388(10059):2519–2531.

doi:10.1016/S0140-6736(16)00576-6

5. Main E, Prasad A. Airway clearance techniques in children and adolescents with

chronic suppurative lung disease and bronchiectasis. Paediatr Respir Rev.

2020;35:40–45.

6. Konstan MW, et al. Therapies aimed at the basic defect in cystic fibrosis. Pediatr

Pulmonol. 2017;52(S48):S42–S55.

7. Clinical case reports archive, Toshkent pediatriya tibbiyot instituti, 2023-yilgi

kuzatuvlar natijasi.

Published

2025-05-16

How to Cite

Karimkulova Gulshonoy Akmaljon qizi. (2025). MUKOVISTSIDOZ KASALLIGIDA NAFAS TIZIMI FAOLIYATINING BUZILISHI VA UNI REABILITATSIYA QILISH USULLARI . Ta’lim Innovatsiyasi Va Integratsiyasi, 45(2), 113-115. https://scientific-jl.com/tal/article/view/13981